Scimitar Syndrome A Rare but Important Condition to Diagnose
نویسنده
چکیده
Scimitar syndrome is a rare but well defined disorder, involving anomalies of lung and pulmonary vein1. Children may present with tachypnea early in life or with repeated chest infection at any age. It is important to diagnose or at least to rule the syndrome as management depends upon the severity of different components. Treatment may be medical, surgical or combined in majority of cases. A case is described here which was fully investigated and family was counseled regarding disease, its prognosis and long term management.
منابع مشابه
Scimitar Syndrome: Pathology, Clinical Presentation, Radiographic Features, and Treatment
Scimitar syndrome is characterized by partial or total anomalous pulmonary venous return from the right lung along with pulmonary hypoplasia.Wesearched the mail databases such as Medline (via PubMed), Scopus and EMBASE and Google Scholar. Diagnosing infantile scimitar syndrome requires meticulous attention and high suspicion of the early referral and management. The association of the syndrome ...
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